Kawasaki disease

MeSH: D009080ORPHA: 2331

Overview

human disease in which blood vessels throughout the body become inflamed

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Kawasaki disease, sourced from HPO and Orphanet clinical annotations.

ArthritisAbnormal heart valve morphologyPericarditisThrombocytosisFeverIncreased total leukocyte countDiarrheaAbdominal painHypoalbuminemiaElevated erythrocyte sedimentation rateElevated circulating C-reactive protein concentrationFatigueScaling skin on fingertipPlantar edemaPalmar edemaConjunctival hyperemiaStrawberry tongueLip fissureAbnormality of nail colorPtosisIrritabilityJaundiceCholecystitisMeningitisCongestive heart failureNausea and vomitingProteinuriaConjunctivitisSkin rashVasculitisCervical lymphadenopathyPalmoplantar erythemaRecurrent pharyngitisCheilitisGlossitisEdemaMigraineArthralgiaAscending tubular aorta aneurysmAbnormal pulmonary interstitial morphologyCranial nerve paralysisDouble outlet right ventricle with subpulmonary ventricular septal defect without pulmonary stenosisArrhythmiaHepatitisMyocarditisSterile pyuria

Classification & Codes

MeSH Code

D009080

Orphanet Code

ORPHA:2331
Kawasaki disease
MeSHD009080
OrphanetORPHA:2331
Treatments0 drug(s)
Symptoms on record46 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO