Kjer's optic neuropathy

ORPHA: 98673

Overview

medical condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Kjer's optic neuropathy, sourced from HPO and Orphanet clinical annotations.

Visual impairmentOptic atrophySensorineural hearing impairmentColor vision defectOphthalmoplegiaSensorimotor neuropathyTemporal optic disc pallorMorning glory anomalyModerately reduced visual acuityPtosisCentral scotomaAtaxiaGait disturbanceMyopathyHypogonadismCataractNystagmusDementiaHallucinationsDiabetes mellitusHypothyroidismSeizureSpasticitySpastic paraplegiaGlobal developmental delayHemiparesisCerebellar atrophyAreflexiaPes cavusMacrocytic anemiaDysphagiaMigraineBasal ganglia calcificationAbnormal periventricular white matter morphologySkeletal muscle atrophyMyalgiaScapular wingingAtrophy/Degeneration affecting the brainstemCorpus callosum atrophyDuane anomalyFeeding difficultiesFatigueWeakness of facial musculatureCognitive impairment

Classification & Codes

Orphanet Code

ORPHA:98673
Kjer's optic neuropathy
OrphanetORPHA:98673
Treatments0 drug(s)
Symptoms on record44 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO