Kostmann syndrome

ICD-10: D70MeSH: C537592ORPHA: 99749

Overview

group of diseases that affect myelopoiesis, causing a congenital form of neutropenia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

D70

MeSH Code

C537592

Orphanet Code

ORPHA:99749
Kostmann syndrome
ICD-10D70
MeSHC537592
OrphanetORPHA:99749
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO