L1 syndrome

MeSH: C536029ORPHA: 2466

Overview

hereditary spastic paraplegia that is characterized by hydrocephalus, spasticity of the lower limbs, adducted thumbs, aphasia, seizures, agenesis of the corpus callosum and intellectual disability in the mild to moderate range

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with L1 syndrome, sourced from HPO and Orphanet clinical annotations.

Delayed speech and language developmentIntellectual disabilityHand clenchingSpastic paraplegiaAgenesis of corpus callosumGait disturbanceHyperreflexiaVentriculomegalyAphasiaClinodactyly of the 5th fingerShort statureHemiplegia/hemiparesisCamptodactyly of finger

Classification & Codes

MeSH Code

C536029

Orphanet Code

ORPHA:2466
L1 syndrome
MeSHC536029
OrphanetORPHA:2466
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO