lamellar ichthyosis

ICD-10: Q80.2MeSH: D017490ORPHA: 313

Overview

disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with lamellar ichthyosis, sourced from HPO and Orphanet clinical annotations.

EctropionDry skinHyperkeratosisPruritusErythrodermaAbnormal nail morphologyIchthyosisSparse hairLack of skin elasticityAplasia/Hypoplasia of the eyebrowEverted lower lip vermilionAbnormal helix morphologyRenal insufficiencyAbnormality of the dentitionChronic otitis mediaDehydrationRecurrent respiratory infectionsShort statureCognitive impairmentGangreneSepsis

Classification & Codes

ICD-10 Code

Q80.2

MeSH Code

D017490

Orphanet Code

ORPHA:313
lamellar ichthyosis
ICD-10Q80.2
MeSHD017490
OrphanetORPHA:313
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO