Larsen syndrome

MeSH: C580241ORPHA: 503

Overview

autosomal dominant disease that is characterized by large-joint dislocations and characteristic craniofacial abnormalities

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Larsen syndrome, sourced from HPO and Orphanet clinical annotations.

CryptorchidismCleft palateMalar flatteningHypertelorismConductive hearing impairmentBrachydactylyIntellectual disabilityCraniosynostosisAbnormality of the cardiovascular systemShort nailRespiratory insufficiencyScoliosisAbnormality of the cervical spineVertebral segmentation defectAccessory carpal bonesShort statureLarge joint dislocationsDepressed nasal bridgeAbnormal epiphysis morphologyFinger syndactylyLaryngotracheomalaciaBroad distal phalanx of fingerShort distal phalanx of fingerProminent foreheadBroad thumbFlat faceJoint hypermobility

Classification & Codes

MeSH Code

C580241

Orphanet Code

ORPHA:503
Larsen syndrome
MeSHC580241
OrphanetORPHA:503
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO