leukoencephalopathy-metaphyseal chondrodysplasia syndrome

MeSH: C567065ORPHA: 83629

Overview

genetic human disorder

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with leukoencephalopathy-metaphyseal chondrodysplasia syndrome, sourced from HPO and Orphanet clinical annotations.

LeukoencephalopathyMetaphyseal chondrodysplasiaVisual impairmentAbnormal optic nerve morphologyIntellectual disabilitySpastic paraplegiaGait disturbanceTremorHyperreflexiaCerebral atrophyAbnormal pyramidal tract morphologyHypoplasia of the corpus callosumEnlargement of the wristsBabinski signReduced bone mineral densityAbnormal brainstem MRI signal intensityTip-toe gaitLarge kneeAbnormal astrocyte morphologyAnteverted naresHorizontal nystagmusDepressed nasal bridgeMidface retrusion

Classification & Codes

MeSH Code

C567065

Orphanet Code

ORPHA:83629
leukoencephalopathy-metaphyseal chondrodysplasia syndrome
MeSHC567065
OrphanetORPHA:83629
Treatments0 drug(s)
Symptoms on record23 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
leukoencephalopathy-metaphyseal chondrodysplasia syndrome | OrphanDrug