Limb deficiencies distal with micrognathia

ORPHA: 1307

Overview

congenital genetic disorder which causes oligodactyly and micrognathia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Limb deficiencies distal with micrognathia, sourced from HPO and Orphanet clinical annotations.

Posteriorly rotated earsMicroretrognathiaHypoplasia of the maxillaAbnormality of chromosome segregationAbnormality of the ankleAbnormal metacarpal morphologyOligodactylyCryptorchidismRenal insufficiencyRenal hypoplasiaProteinuriaNarrow mouthHigh palateConductive hearing impairmentMyopiaModerate intellectual disabilityAbnormality of the wristAplasia/Hypoplasia of the radiusAplasia/Hypoplasia of the thumbMicroglossiaCleft palateMacrocephalySensorineural hearing impairmentProminent nasal bridgeNystagmusMicrodontiaSplit footShort statureTarsal synostosisAbnormal morphology of ulna

Classification & Codes

Orphanet Code

ORPHA:1307
Limb deficiencies distal with micrognathia
OrphanetORPHA:1307
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Limb deficiencies distal with micrognathia | OrphanDrug