linear IgA bullous dermatosis

MeSH: D062027ORPHA: 46488

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with linear IgA bullous dermatosis, sourced from HPO and Orphanet clinical annotations.

AutoimmunityAbnormal blistering of the skinPapuleOral ulcerAnti-LAD-1 antibody positivityAnti-LABD97 antibody positivityEpistaxisPruritusInflammation of the large intestineBladder neoplasmRenal neoplasm

Classification & Codes

MeSH Code

D062027

Orphanet Code

ORPHA:46488
linear IgA bullous dermatosis
MeSHD062027
OrphanetORPHA:46488
Treatments0 drug(s)
Symptoms on record11 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO