localized junctional epidermolysis bullosa, non-Herlitz type

ORPHA: 251393

Overview

Junctional epidermolysis bullosa, localized non-Herlitz-type is a form of non-Herlitz junctional epidermolysis bullosa (JEB-nH, see this term) characterized by localized blistering, and dystrophic or absent nails

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with localized junctional epidermolysis bullosa, non-Herlitz type, sourced from HPO and Orphanet clinical annotations.

Fragile skinAbnormal blistering of the skinSparse axillary hairSparse pubic hairAtrophic, patchy alopeciaEnamel hypoplasiaNail dystrophyDental enamel pitsAbnormality of dental colorAcral blisteringSkin detachmentAplasia cutis congenitaDystrophic toenailScarring alopecia of scalpDystrophic fingernailsAtypical scarring of skinMiliaLimb joint contractureMitten deformity

Classification & Codes

Orphanet Code

ORPHA:251393
localized junctional epidermolysis bullosa, non-Herlitz type
OrphanetORPHA:251393
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO