Loeys-Dietz syndrome 2

ORPHA: 558

Overview

Loeys-Dietz syndrome that has material basis in heterozygous mutation in the TGFBR2 gene on chromosome 3p24

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Loeys-Dietz syndrome 2, sourced from HPO and Orphanet clinical annotations.

Disproportionate tall statureSlender buildPes planusSpontaneous pneumothoraxAortic root aneurysmAortic aneurysmChronic fatigueNarrow faceVisual impairmentMyopiaDental crowdingPectus excavatumEctopia lentisLens subluxationJoint hypermobilityMitral valve prolapseMitral regurgitationAortic regurgitationTricuspid valve prolapseSleep disturbanceAortic dissectionScoliosisHigh, narrow palateProtrusio acetabuliAscending tubular aorta aneurysmArthralgia/arthritisIncreased axial length of the globeSleep apneaAbnormal zygomatic bone morphologyLens luxationDural ectasiaInguinal herniaCleft palateDolichocephalyRetrognathiaMicrognathiaDownslanted palpebral fissuresGlaucomaRetinal detachmentOsteopeniaOsteoporosisHypotoniaCongestive heart failureEmphysemaHemoptysisMeningoceleDilatation of an abdominal arteryKyphosisLimited elbow movementSkeletal muscle atrophySpondylolisthesisMyalgiaCachexiaReduced bone mineral densityMitral valve calcificationVentricular tachycardiaPulmonary artery dilatationAbnormal left ventricular functionArterial dissectionAortic tortuosityAttention deficit hyperactivity disorderHypoplasia of the irisFlat corneaOpen biteInsomniaPectus carinatumStriae distensaeArachnodactyly

Classification & Codes

Orphanet Code

ORPHA:558
Loeys-Dietz syndrome 2
OrphanetORPHA:558
Treatments0 drug(s)
Symptoms on record68 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO