lymphedema-cerebral arteriovenous anomaly syndrome

MeSH: C563612ORPHA: 86914

Overview

Lymphedema-cerebral arteriovenous anomaly syndrome is characterised by the variable association of a cerebrovascular malformation, foot lymphoedema and primary pulmonary hypertension. It has been described in a woman and four of her children.

Available Treatments (0)

No treatments linked yet

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Classification & Codes

MeSH Code

C563612

Orphanet Code

ORPHA:86914
lymphedema-cerebral arteriovenous anomaly syndrome
MeSHC563612
OrphanetORPHA:86914
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO