lymphoid interstitial pneumonia
ORPHA: 79128
Overview
Human disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with lymphoid interstitial pneumonia, sourced from HPO and Orphanet clinical annotations.
CoughEczematoid dermatitisClubbingFailure to thriveRestrictive ventilatory defectDyspneaAutoimmunityMultiple pulmonary cystsFatigueHypoxemiaGround-glass opacificationAutoimmune antibody positivityWheezingCracklesSevere viral infectionParenchymal consolidationDecreased DLCOEnlarged kidneySkin rashKeratoconjunctivitis siccaRheumatoid arthritisWeight lossFeverBronchiectasisHepatomegalyImmunodeficiencyAbnormality of connective tissueRespiratory tract infectionSubpleural interstitial thickeningCentrilobular ground-glass opacification on pulmonary HRCTRaynaud phenomenonPulmonary venous hypertensionMediastinal lymphadenopathyPulmonary fibrosis
Classification & Codes
Orphanet Code
ORPHA:79128lymphoid interstitial pneumonia
| Orphanet | ORPHA:79128 |
| Treatments | 0 drug(s) |
| Symptoms on record | 34 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO