macrocephaly, dysmorphic facies, and psychomotor retardation

ORPHA: 457359

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with macrocephaly, dysmorphic facies, and psychomotor retardation, sourced from HPO and Orphanet clinical annotations.

MegalencephalyDisproportionate tall statureLarge for gestational ageSlender buildLong footAbnormal facial shapeGait ataxiaBilateral tonic-clonic seizureDroolingKyphoscoliosisMicropenisMalar flatteningFacial hypotoniaTriangular faceProminent nasal bridgeLong neckShallow orbitsCerebellar hypoplasiaCommunicating hydrocephalusLimitation of joint mobilityJoint hypermobilityAsymmetry of the thoraxPes planusNeonatal hypoglycemiaVentriculomegalyCerebral cortical atrophyKyphosisLumbar hyperlordosisSevere expressive language delayThick corpus callosumDiffuse white matter abnormalitiesHigh myopiaMetopic synostosisReduced social responsivenessLong faceHypertelorismArachnodactylyHypotoniaOvergrowthSevere intellectual disabilityProminent foreheadBroad eyebrowSparse eyebrowHigh palateMacrocephalyMandibular prognathiaPosteriorly rotated earsMacrotiaDownslanted palpebral fissuresProptosisUpslanted palpebral fissureGlobal developmental delayGait disturbanceAbsent speech

Classification & Codes

Orphanet Code

ORPHA:457359
macrocephaly, dysmorphic facies, and psychomotor retardation
OrphanetORPHA:457359
Treatments0 drug(s)
Symptoms on record54 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO