macrophage activation syndrome
MeSH: D055501ORPHA: 158061
Overview
complication of several chronic rheumatic diseases of childhood
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with macrophage activation syndrome, sourced from HPO and Orphanet clinical annotations.
Decreased liver functionThrombocytopeniaAnemiaFeverAutoimmunityHypoalbuminemiaIncreased circulating ferritin concentrationElevated erythrocyte sedimentation rateAbnormal circulating interleukin concentrationAbnormality of tumor necrosis factor secretionHemophagocytosisIncreased inflammatory responseIncreased circulating lactate dehydrogenase concentrationIncreased circulating interferon-gamma concentrationIncreased circulating interleukin 6 concentrationElevated circulating alanine aminotransferase concentrationAbnormal total natural killer cell countSplenomegalyDecreased total neutrophil countHypertriglyceridemiaLymphadenopathyJuvenile rheumatoid arthritisElevated circulating C-reactive protein concentrationHypofibrinogenemiaElevated circulating aspartate aminotransferase concentrationEncephalopathyHepatomegalySystemic lupus erythematosusHepatitis
Classification & Codes
MeSH Code
D055501Orphanet Code
ORPHA:158061macrophage activation syndrome
| MeSH | D055501 |
| Orphanet | ORPHA:158061 |
| Treatments | 0 drug(s) |
| Symptoms on record | 29 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO