male hypergonadotropic hypogonadism-intellectual disability-skeletal anomalies syndrome

ORPHA: 2234

Overview

This syndrome is characterized by hypergonadotropic hypogonadism, intellectual deficit, congenital skeletal anomalies involving the cervical spine and superior ribs, and diabetes mellitus

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with male hypergonadotropic hypogonadism-intellectual disability-skeletal anomalies syndrome, sourced from HPO and Orphanet clinical annotations.

Small scrotumHypogonadismDecreased fertilityAtypical behaviorGynecomastiaIntellectual disabilityHemivertebraeAbnormal form of the vertebral bodiesEunuchoid habitusType II diabetes mellitusDecreased testicular sizeHypoplasia of penisShort neckAbnormal rib morphologyAbnormality of the thyroid glandObesitySparse body hairShort statureAbnormality of the humeroulnar joint

Classification & Codes

Orphanet Code

ORPHA:2234
male hypergonadotropic hypogonadism-intellectual disability-skeletal anomalies syndrome
OrphanetORPHA:2234
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
male hypergonadotropic hypogonadism-intellectual disability-skeletal anomalies syndrome | OrphanDrug