mandibuloacral dysplasia with type A lipodystrophy

ORPHA: 90153

Available Treatments (0)

No treatments linked yet

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Clinical Presentation

Signs and symptoms associated with mandibuloacral dysplasia with type A lipodystrophy, sourced from HPO and Orphanet clinical annotations.

Abnormality of the dentitionHigh palateLarge fontanellesHearing impairmentCataractProptosisAbnormal eyebrow morphologyAbsent eyelashesInsulin resistanceHyperpigmentation of the skinThin skinHypotoniaFlexion contractureLimitation of joint mobilityAlopeciaAcroosteolysis of distal phalanges (feet)Wormian bonesOsteolysisArthralgiaAbnormality of the musculatureHyperlipidemiaShort statureDermal atrophyProgeroid facial appearanceAplasia/Hypoplasia of the claviclesPrematurely aged appearanceOsteolytic defects of the distal phalanges of the handShort distal phalanx of fingerLack of skin elasticityBreast aplasia

Classification & Codes

Orphanet Code

ORPHA:90153
mandibuloacral dysplasia with type A lipodystrophy
OrphanetORPHA:90153
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO