Mannosidosis

MeSH: D044904ORPHA: 61

Overview

Lysosomal storage disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Mannosidosis, sourced from HPO and Orphanet clinical annotations.

MacroglossiaCoarse facial featuresHearing impairmentCataractIntellectual disabilityGlobal developmental delaySplenomegalyHepatomegalySkeletal dysplasiaDelayed skeletal maturationCraniofacial hyperostosisDepressed nasal bridgeType II diabetes mellitusCorneal opacityHypoplastic inferior iliaInguinal herniaNarrow palateGingival overgrowthHypertelorismProminent supraorbital ridgesChronic otitis mediaMacrotiaShort neckAtypical behaviorHypotoniaHip dysplasiaScoliosisKyphosisBowing of the long bonesOpen biteAbnormal helix morphologyGeneralized abnormality of skinMacrocephalyMandibular prognathiaWidely spaced teethDental malocclusionHallucinationsArthritisRecurrent respiratory infectionsIncreased intracranial pressureAvascular necrosisSynostosis of joints

Classification & Codes

MeSH Code

D044904

Orphanet Code

ORPHA:61
Mannosidosis
MeSHD044904
OrphanetORPHA:61
Treatments0 drug(s)
Symptoms on record42 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO