Marchiafava-Bignami disease
ICD-10: G37.1MeSH: D054319ORPHA: 221074
Overview
medical condition
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Marchiafava-Bignami disease, sourced from HPO and Orphanet clinical annotations.
Abnormal corpus callosum morphologyMalnutritionAddictive alcohol useDecreased circulating vitamin B1 concentrationComaDysarthriaGait disturbanceGait ataxiaHeadacheMemory impairmentLimb hypertoniaLoss of consciousnessCNS demyelinationCognitive impairmentAbnormal emotional stateUrinary incontinenceAbnormality of visionOphthalmoplegiaNystagmusDiplopiaAtypical behaviorPsychosisDepressionAggressive behaviorDementiaApathyDelusionSeizureAtaxiaExcessive daytime somnolenceHemiparesisConfusionVomitingRigidityAbnormal basal ganglia morphologyApraxiaTetraparesisMutismVertigoVisual hallucinationAphasiaPrimitive reflexIncreased CSF protein concentrationAbnormal pyramidal signDyslexiaDysgraphiaFacial palsyAnomic aphasiaDeliriumFever
Classification & Codes
ICD-10 Code
G37.1MeSH Code
D054319Orphanet Code
ORPHA:221074Marchiafava-Bignami disease
| ICD-10 | G37.1 |
| MeSH | D054319 |
| Orphanet | ORPHA:221074 |
| Treatments | 0 drug(s) |
| Symptoms on record | 50 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO