marfanoid habitus-autosomal recessive intellectual disability syndrome

MeSH: C565410ORPHA: 2463

Available Treatments (0)

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Clinical Presentation

Signs and symptoms associated with marfanoid habitus-autosomal recessive intellectual disability syndrome, sourced from HPO and Orphanet clinical annotations.

Tall statureGlobal developmental delayJoint hypermobilityDisproportionate tall statureSlender long boneEunuchoid habitusIncreased arm spanNarrow mouthHigh palateDolichocephalyMalar flatteningCoarse facial featuresHypertelorismMacrotiaWide nosePectus excavatumThin ribsOsteopeniaArachnodactylyHypotoniaLong footThenar muscle atrophyThin metacarpal corticesAbnormality of the palpebral fissuresThin metatarsal corticesHypoplasia of the musculatureAbnormal columella morphologySmall hypothenar eminenceBroad chinAbnormal bone ossificationSubcortical cerebral atrophyFlat faceBroad philtrumEsotropiaSynophrysAbnormal thymus morphologyHirsutismCardiomegalyLow posterior hairlineDelayed skeletal maturationLumbar hemivertebraeLoss of truncal subcutaneous adipose tissueMucosal telangiectasiae

Classification & Codes

MeSH Code

C565410

Orphanet Code

ORPHA:2463
marfanoid habitus-autosomal recessive intellectual disability syndrome
MeSHC565410
OrphanetORPHA:2463
Treatments0 drug(s)
Symptoms on record43 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO