MASS syndrome

ICD-10: Q87.5MeSH: C536030ORPHA: 85194

Overview

Connective tissue disorder

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with MASS syndrome, sourced from HPO and Orphanet clinical annotations.

Thin vermilion borderFacial hypotoniaHypertelorismLong philtrumLow-set earsThickened helicesWebbed neckShort neckCataractAbnormal eyebrow morphologyRetinal detachmentMyopiaMicrophthalmiaVisual lossNystagmusPlatyspondylyOsteoporosisHyperextensible skinIntellectual disabilityVentricular septal defectPes planusLow posterior hairlineThoracic kyphosisDisproportionate short-trunk short statureShort staturePreauricular pitAbnormal intervertebral disk morphologyIris hypopigmentationAplasia/Hypoplasia of the lensAbnormal antihelix morphologyJoint hypermobility

Classification & Codes

ICD-10 Code

Q87.5

MeSH Code

C536030

Orphanet Code

ORPHA:85194
MASS syndrome
ICD-10Q87.5
MeSHC536030
OrphanetORPHA:85194
Treatments0 drug(s)
Symptoms on record31 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
MASS syndrome | OrphanDrug