maternally-inherited cardiomyopathy and hearing loss

ORPHA: 1349

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with maternally-inherited cardiomyopathy and hearing loss, sourced from HPO and Orphanet clinical annotations.

Sensorineural hearing impairmentAtaxiaGait disturbanceMuscle weaknessSlurred speechHypertrophic cardiomyopathyMild global developmental delayProgressive external ophthalmoplegiaOphthalmoparesisMental deteriorationEncephalopathyCongestive heart failureDilated cardiomyopathyDyspneaIncreased circulating lactate concentrationRagged-red muscle fibersEMG abnormalityIncreased circulating pyruvate concentrationExercise intoleranceLower limb painAbnormal cardiovascular system morphologyHypertensionMultiple lipomasHyperreflexiaFebrile seizure (within the age range of 3 months to 6 years)MyalgiaIncreased adipose tissuePeripheral neuropathyFatigueChest pain

Classification & Codes

Orphanet Code

ORPHA:1349
maternally-inherited cardiomyopathy and hearing loss
OrphanetORPHA:1349
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO