medullary cystic kidney disease

ICD-10: Q61.5ORPHA: 34149

Overview

inherited form of cystic kidney disease leading to fibrosis and impaired renal function that is caused by mutations in the UMOD gene, which encodes uromodulin/Tamm-Horsfall mucoprotein

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

Q61.5

Orphanet Code

ORPHA:34149
medullary cystic kidney disease
ICD-10Q61.5
OrphanetORPHA:34149
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO