MEND syndrome

ORPHA: 401973

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with MEND syndrome, sourced from HPO and Orphanet clinical annotations.

Elevated 8-dehydrocholesterolElevated 8(9)-cholestenolCryptorchidismHigh palateHydrocephalusWide anterior fontanelHypertelorismMicrognathiaLow-set earsAbnormal nasal bridge morphologyProminent nasal bridgeLong neckThickened nuchal skin foldTelecanthusCataractMicrophthalmiaUpslanted palpebral fissureSacral dimpleHand polydactylyIntellectual disabilitySeizureGlobal developmental delayGeneralized hypotoniaDandy-Walker malformationFailure to thriveAortic valve stenosisOverlapping toeHypoplasia of the corpus callosumLimb hypertoniaKyphosisShort stature2-3 toe syndactylySpotty hypopigmentationAbnormal auditory evoked potentialsIchthyosisAsymmetry of the mouthBroad halluxOverlapping fingersMidface retrusionAbnormal social behaviorLong fingersCleft palateAggressive behaviorHyperactivityAbnormal heart morphology

Classification & Codes

Orphanet Code

ORPHA:401973
MEND syndrome
OrphanetORPHA:401973
Treatments0 drug(s)
Symptoms on record45 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO