metachromatic leukodystrophy, juvenile form

ORPHA: 309263

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with metachromatic leukodystrophy, juvenile form, sourced from HPO and Orphanet clinical annotations.

Urinary incontinenceOptic atrophyShort attention spanDecreased nerve conduction velocityDysarthriaHyporeflexiaGeneralized hypotoniaMuscle weaknessDystoniaClumsinessFrequent fallsDevelopmental regressionLeukodystrophyIncreased CSF protein concentrationAbnormal glycosphingolipid metabolismAbnormal social behaviorPunctate periventricular T2 hyperintense fociAbnormality of visual evoked potentialsEmotional labilityHallucinationsDelusionCholecystitisSeizureSpasticityAbnormality of metabolism/homeostasisIntention tremorLoss of speechAbdominal distentionEMG: chronic denervation signsBabinski signProgressive peripheral neuropathyProgressive gait ataxiaProgressive psychomotor deteriorationReduced visual acuityBilateral sensorineural hearing impairmentDecerebrate rigidityVegetative state

Classification & Codes

Orphanet Code

ORPHA:309263
metachromatic leukodystrophy, juvenile form
OrphanetORPHA:309263
Treatments0 drug(s)
Symptoms on record37 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO