microcephaly-cardiac defect-lung malsegmentation syndrome

ORPHA: 2516

Overview

Microcephaly - cardiac defect - lung malsegmentation syndrome is a very rare syndrome characterized by the combination of microcephaly, heart defects, renal hypoplasia, lung segmentation defects and cleft palate

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with microcephaly-cardiac defect-lung malsegmentation syndrome, sourced from HPO and Orphanet clinical annotations.

MicrocephalyIntrauterine growth retardationVentricular septal defectAbnormal lung lobationCognitive impairmentRenal agenesisCleft palateMicrognathiaAbnormal periauricular region morphologyUnderdeveloped nasal alaeWebbed neckShort neckBlepharophimosisHypotoniaJoint stiffnessTruncus arteriosusAbnormal aortic morphologyHigh, narrow palatePreauricular pitWide intermamillary distanceBilateral single transverse palmar creasesRenal hypoplasia/aplasiaShort distal phalanx of finger

Classification & Codes

Orphanet Code

ORPHA:2516
microcephaly-cardiac defect-lung malsegmentation syndrome
OrphanetORPHA:2516
Treatments0 drug(s)
Symptoms on record23 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO