microcephaly-polymicrogyria-corpus callosum agenesis syndrome

ORPHA: 171703

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with microcephaly-polymicrogyria-corpus callosum agenesis syndrome, sourced from HPO and Orphanet clinical annotations.

Agenesis of corpus callosumCerebellar hypoplasiaRespiratory distressVentriculomegalyPolymicrogyriaRecurrent infectionsPrimary microcephaly

Classification & Codes

Orphanet Code

ORPHA:171703
microcephaly-polymicrogyria-corpus callosum agenesis syndrome
OrphanetORPHA:171703
Treatments0 drug(s)
Symptoms on record7 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO