microgastria-limb reduction defect syndrome

MeSH: C537554ORPHA: 2538

Overview

This syndrome is characterised by the association of microgastria with a limb reduction defect

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with microgastria-limb reduction defect syndrome, sourced from HPO and Orphanet clinical annotations.

Failure to thriveGrowth delayAbnormality of the spleenGastroesophageal refluxHiatus herniaAbnormal morphology of the radiusShort thumbFeeding difficultiesEsophagitisMicrogastriaMulticystic kidney dysplasiaRenal dysplasiaAbnormal finger morphologyPlagiocephalyFrontal bossingAbnormal metacarpal morphologyCongenital muscular torticollisProminent foreheadHorseshoe kidneyRenal agenesisRectovaginal fistulaAnophthalmiaMicrophthalmiaAgenesis of corpus callosumAbsent septum pellucidumAtrial septal defectTruncus arteriosusAnal atresiaEsophageal atresiaAbnormal lung lobationArrhinencephalyHepatomegalyAbnormal cortical gyrationIntestinal malrotationTracheoesophageal fistulaElbow dislocationAbsent handCrossed fused renal ectopiaPerineal fistulaAplastic clavicleRenal hypoplasia/aplasiaAmeliaPhocomeliaOligodactylyRectal atresiaAbnormal cardiovascular system morphologyEctrodactylyAbnormal humerus morphology

Classification & Codes

MeSH Code

C537554

Orphanet Code

ORPHA:2538
microgastria-limb reduction defect syndrome
MeSHC537554
OrphanetORPHA:2538
Treatments0 drug(s)
Symptoms on record48 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO