microscopic polyangiitis
ICD-10: M31.7MeSH: D055953ORPHA: 727
Overview
inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels in multiple organs
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with microscopic polyangiitis, sourced from HPO and Orphanet clinical annotations.
Renal insufficiencyGlomerulonephritisHematuriaSkin rashFeverHemoptysisVasculitisAutoimmunityCrescentic glomerulonephritisErythemaIncreased inflammatory responseOliguriaGlomerulopathyAnemiaSubcutaneous hemorrhageDiarrheaNausea and vomitingAbdominal painGastrointestinal hemorrhagePeritonitisArthralgiaMyalgiaElevated erythrocyte sedimentation ratePoor appetiteVenous thrombosisGastrointestinal infarctionsFatigueAbnormal urine cytologyMultiple mononeuropathyCytoplasmic antineutrophil antibody positivityLivedo reticularisAnti-proteinase 3 antibody positivityAnti-myeloperoxidase antibody positivityAnti-neutrophil elastase antibody positivitySkin ulcerSinusitisEpistaxisUveitisCutis marmorataArthritisSubcutaneous noduleCongestive heart failurePericarditisPancreatitisWeight lossParesthesiaAbnormal retinal vascular morphologyPeripheral neuropathyArrhythmiaRetinal vasculitisDiffuse alveolar hemorrhagePalpable purpuraEpiscleritisChest painGangreneInflammation
Classification & Codes
ICD-10 Code
M31.7MeSH Code
D055953Orphanet Code
ORPHA:727microscopic polyangiitis
| ICD-10 | M31.7 |
| MeSH | D055953 |
| Orphanet | ORPHA:727 |
| Treatments | 0 drug(s) |
| Symptoms on record | 56 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO