mixed connective tissue disease

MeSH: D008947ORPHA: 809

Overview

collagen disease that is considered an overlap of three diseases, systemic lupus erythematosus, scleroderma, and polymyositis with very high titers of circulating antinuclear antibody to a ribonucleoprotein antigen

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with mixed connective tissue disease, sourced from HPO and Orphanet clinical annotations.

FeverPleuritisArthralgiaRheumatoid factor positiveEdema of the dorsum of handsIncreased circulating immunoglobulin concentrationSclerodactylyAnti-dsDNA antibody positivityRaynaud phenomenonAnti-U1 ribonucleoprotein antibody positivityAnti-ribosome Po antibody positivityAnti-cyclic citrullinated peptide antibody positivityAnti-Ro52/TRIM21 antibody positivityMyositisTrigeminal neuralgiaProteinuriaSkin rashArthritisGastroesophageal refluxDyspneaPulmonary fibrosisAutoimmunityMyalgiaElevated erythrocyte sedimentation rateGastritisFatigueSclerodermaChest painXerostomiaPsychosisKeratoconjunctivitis siccaJoint swellingNephropathyOral ulcerHearing impairmentDepressionPurpuraTelangiectasiaSeizureJoint stiffnessAlopeciaPericardial effusionPericarditisSplenomegalyThrombocytopeniaHemolytic anemiaDecreased total leukocyte countPulmonary arterial hypertensionGastrointestinal hemorrhageHeadacheLymphadenopathyOsteolysisProlonged bleeding timeHypoproteinemiaAbnormal EKGAbnormal pulmonary interstitial morphologyPeripheral neuropathyAvascular necrosisAnasarcaErythema nodosumMembranous nephropathyMyocarditisMalar rashAbnormality on pulmonary function testingIneffective esophageal peristalsisNon-infectious meningitisMalaiseMediastinal lymphadenopathy

Classification & Codes

MeSH Code

D008947

Orphanet Code

ORPHA:809
mixed connective tissue disease
MeSHD008947
OrphanetORPHA:809
Treatments0 drug(s)
Symptoms on record68 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO