monosomy 22

ORPHA: 96123

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with monosomy 22, sourced from HPO and Orphanet clinical annotations.

Posteriorly rotated earsOpen mouthHigh palateThin vermilion borderProminent occiputRetrognathiaEpicanthusLong philtrumHigh foreheadWide noseShort neckAbnormality of the periorbital regionSynophrysSingle transverse palmar creaseIntellectual disabilityMeningiomaClinodactyly of the 5th fingerFlat faceNarrow palpebral fissureSchwannomaSarcomaMicropenisMicrocephalyHyperhidrosisSeborrheic dermatitisThickened skinClubbingHypertoniaJoint swellingHepatosplenomegalyHypochromic microcytic anemiaProminent nasolabial foldAplasia of the thymusContractures of the large jointsFinger syndactylyAbnormal blistering of the skinSparse hairCutis gyrata of scalpGonadal neoplasmScleroderma

Classification & Codes

Orphanet Code

ORPHA:96123
monosomy 22
OrphanetORPHA:96123
Treatments0 drug(s)
Symptoms on record40 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO