multiple acyl-CoA dehydrogenase deficiency

MeSH: D054069ORPHA: 26791

Overview

medical condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with multiple acyl-CoA dehydrogenase deficiency, sourced from HPO and Orphanet clinical annotations.

HypotoniaHypoglycemiaElevated circulating creatine kinase concentrationMyalgiaProximal muscle weaknessExercise-induced muscle fatiguePhenotypic abnormalityWide anterior fontanelHigh foreheadAbnormal pinna morphologyTelecanthusAbnormality of the skeletal systemSeizureAreflexiaDecreased liver functionAbnormal heart morphologyCongestive heart failureMetabolic acidosisHyperammonemiaVomitingDysphagiaDyspneaHepatomegalyHepatic periportal necrosisRespiratory failureElevated circulating hepatic transaminase concentrationLactic acidosisGlutaric aciduriaSkeletal muscle atrophyEthylmalonic aciduriaDecreased circulating carnitine concentrationHyperlordosis3-Methylglutaric aciduriaExercise intoleranceDifficulty climbing stairsLacticaciduriaDepressed nasal bridgeFeeding difficultiesIncreased intramyocellular lipid dropletsIncreased circulating lactate dehydrogenase concentrationFatigable weakness of neck musclesElevated circulating acylcarnitine concentrationAbnormality of the genital systemPolycystic kidney dysplasiaMacrocephalyEncephalopathyCardiomyopathyAcute pancreatitisRestrictive ventilatory defectGliosisGray matter heterotopiaPoor head controlInability to walkRhabdomyolysisScapular wingingCardiorespiratory arrestReye syndrome-like episodesArrhythmia

Classification & Codes

MeSH Code

D054069

Orphanet Code

ORPHA:26791
multiple acyl-CoA dehydrogenase deficiency
MeSHD054069
OrphanetORPHA:26791
Treatments0 drug(s)
Symptoms on record58 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO