MYH9-related disorder

ORPHA: 182050

Overview

blood platelet disease that has material basis in mutations in the MYH9 gene. It is characterized by thrombocytopenia, enlarged platelets, sensorineural hearing loss and presenile cataract

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with MYH9-related disorder, sourced from HPO and Orphanet clinical annotations.

Congenital thrombocytopeniaRenal insufficiencyProteinuriaNephropathyNephritisMenorrhagiaSensorineural hearing impairmentBruising susceptibilityGiant plateletsElevated circulating hepatic transaminase concentrationProlonged bleeding timeSpontaneous, recurrent epistaxisPresenile cataractsNeutrophil inclusion bodiesIncreased mean platelet volumeMyocardial infarction

Classification & Codes

Orphanet Code

ORPHA:182050
MYH9-related disorder
OrphanetORPHA:182050
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO