myoglobinuria, acute recurrent, autosomal recessive

MeSH: C564832ORPHA: 99845

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with myoglobinuria, acute recurrent, autosomal recessive, sourced from HPO and Orphanet clinical annotations.

Gait disturbanceRecurrent myoglobinuriaMuscle weaknessFeverHighly elevated creatine kinaseDark urineRenal insufficiencyReduced tendon reflexesElevated circulating hepatic transaminase concentrationType 2 muscle fiber atrophyViral infection-induced rhabdomyolysisExercise-induced myalgiaExercise-induced myoglobinuriaAbnormality of glycolipid metabolismElevated circulating aldolase concentrationIncreased circulating lactate dehydrogenase concentrationMyositisNeck muscle weaknessAcute kidney injuryHyperkalemiaAbnormal speech patternHypocalcemiaHyperphosphatemiaMuscle spasmImpaired masticationLower limb muscle weaknessProximal upper limb muscle weaknessArrhythmiaFatigable weakness of swallowing musclesAbnormality of jaw musclesOliguriaDisseminated intravascular coagulation

Classification & Codes

MeSH Code

C564832

Orphanet Code

ORPHA:99845
myoglobinuria, acute recurrent, autosomal recessive
MeSHC564832
OrphanetORPHA:99845
Treatments0 drug(s)
Symptoms on record32 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO