Nelson syndrome
MeSH: D009347ORPHA: 199244
Overview
hormonal disorder sometimes resulting from adrenal gland removal
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Nelson syndrome, sourced from HPO and Orphanet clinical annotations.
Secondary hypercortisolismAdrenocorticotropic hormone excessIncreased circulating cortisol levelPituitary corticotropic cell adenomaIncreased urinary cortisol levelVisual impairmentHypertensionStriae distensaeHypokalemiaType II diabetes mellitusLower limb muscle weaknessGeneralized hyperpigmentationSlow decrease in visual acuityBitemporal hemianopiaAbnormal kinetic perimetry testAnterior hypopituitarismIncreased intracranial pressureOptic nerve compressionQuadriceps muscle atrophyOculomotor nerve palsyIncreased circulating prolactin concentrationDiabetes insipidusIntracranial hemorrhageTesticular neoplasmPituitary carcinomaOcular painAbnormality of the sphenoid sinus
Classification & Codes
MeSH Code
D009347Orphanet Code
ORPHA:199244Nelson syndrome
| MeSH | D009347 |
| Orphanet | ORPHA:199244 |
| Treatments | 0 drug(s) |
| Symptoms on record | 27 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO