neuroleptic malignant syndrome

ICD-10: G21.0MeSH: D009459ORPHA: 94093

Overview

nervous system disease that is characterized by hyperthermia, muscular rigidity, autonomic dysfunction and altered consciousness and is associated with administration of antipsychotic and other central dopaminergic blockers

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with neuroleptic malignant syndrome, sourced from HPO and Orphanet clinical annotations.

HyperhidrosisFeverMutismReduced consciousnessExtrapyramidal muscular rigidityAbnormal autonomic nervous system physiologyHypertensionTremorTachycardiaMetabolic acidosisIncreased total leukocyte countDysphagiaDroolingElevated circulating creatine kinase concentrationMuscle spasmExcessive salivationFatigueUrinary incontinenceProteinuriaAgitationAnxietyComaEncephalopathyThrombocytosisAcute kidney injuryDehydrationVomitingNauseaChoreaHyperuricemiaHyperkalemiaPulmonary embolismHypotensionHypocalcemiaHyponatremiaHyperphosphatemiaElevated circulating hepatic transaminase concentrationMyoglobinuriaHypomagnesemiaElevated circulating alkaline phosphatase concentrationRhabdomyolysisHypernatremiaOculogyric crisisArrhythmiaAspiration pneumoniaRigorsIncreased circulating lactate dehydrogenase concentrationDeliriumNasogastric tube feedingHypertensive crisisBradycardiaThrombocytopeniaHypothermiaSepsis

Classification & Codes

ICD-10 Code

G21.0

MeSH Code

D009459

Orphanet Code

ORPHA:94093
neuroleptic malignant syndrome
ICD-10G21.0
MeSHD009459
OrphanetORPHA:94093
Treatments0 drug(s)
Symptoms on record54 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO