non-immunoglobulin-mediated membranoproliferative glomerulonephritis
ORPHA: 329918
Overview
human disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with non-immunoglobulin-mediated membranoproliferative glomerulonephritis, sourced from HPO and Orphanet clinical annotations.
HematuriaProteinuriaMembranoproliferative glomerulonephritisHypertensionElevated circulating creatinine concentrationStage 5 chronic kidney diseaseDecreased circulating complement C3 concentrationMesangial hypercellularityChronic kidney diseaseGlomerular extracapillary hypercellularityC3 nephritic factor positivityParaproteinemiaNephrotic syndromeVisual lossAcute kidney injuryRecurrent infectionsAutoimmunityLipodystrophyDrusenCentral serous chorioretinopathyAbnormal dark-adapted electroretinogramYellow/white retinal lesionDecreased circulating complement C4 concentration
Classification & Codes
Orphanet Code
ORPHA:329918non-immunoglobulin-mediated membranoproliferative glomerulonephritis
| Orphanet | ORPHA:329918 |
| Treatments | 0 drug(s) |
| Symptoms on record | 23 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO