NTHL1-related attenuated familial adenomatous polyposis

ORPHA: 454840

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with NTHL1-related attenuated familial adenomatous polyposis, sourced from HPO and Orphanet clinical annotations.

Adenomatous colonic polyposisMeningiomaBreast carcinomaColon cancerNeoplasm of the skinBladder neoplasmEndometrial carcinomaNeoplasm of the rectumOvarian cystBasal cell carcinomaSquamous cell carcinomaPancreatic adenocarcinomaDuodenal adenocarcinomaNon-Hodgkin lymphomaSeborrheic keratosis

Classification & Codes

Orphanet Code

ORPHA:454840
NTHL1-related attenuated familial adenomatous polyposis
OrphanetORPHA:454840
Treatments0 drug(s)
Symptoms on record15 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO