oculocerebral hypopigmentation syndrome of Preus

ORPHA: 2720

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with oculocerebral hypopigmentation syndrome of Preus, sourced from HPO and Orphanet clinical annotations.

Abnormal renal tubule morphologyHigh palateHydrocephalusHearing impairmentCataractPhotophobiaNystagmusOcular albinismArachnodactylyIntellectual disabilitySeizureAtaxiaGlobal developmental delayHypertoniaAbnormality of neutrophilsHypochromic anemiaAbnormal brainstem morphologyAbnormal hip bone morphologyShort statureReduced bone mineral densityAplasia/Hypoplasia of the cerebellumGeneralized hypopigmentationIris hypopigmentationAbnormal diencephalon morphologyAbnormality of immune system physiologyWhite hair

Classification & Codes

Orphanet Code

ORPHA:2720
oculocerebral hypopigmentation syndrome of Preus
OrphanetORPHA:2720
Treatments0 drug(s)
Symptoms on record26 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO