oculomaxillofacial dysostosis

MeSH: C537736ORPHA: 1794

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with oculomaxillofacial dysostosis, sourced from HPO and Orphanet clinical annotations.

Median cleft upper lipAbnormality of the dentitionCleft palateAbnormality of the noseUnderdeveloped nasal alaeWide nasal bridgeAbnormal eyelash morphologyUpslanted palpebral fissureTessier cleftShort statureCorneal opacityAplasia/Hypoplasia of the eyebrowSparse or absent eyelashesMicrognathiaAbnormal eyelid morphologyBrachydactylyAdducted thumbAplasia/Hypoplasia affecting the eyeCamptodactyly of fingerCognitive impairmentAbnormal humerus morphology

Classification & Codes

MeSH Code

C537736

Orphanet Code

ORPHA:1794
oculomaxillofacial dysostosis
MeSHC537736
OrphanetORPHA:1794
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO