oculorenocerebellar syndrome

MeSH: C537739ORPHA: 2715

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with oculorenocerebellar syndrome, sourced from HPO and Orphanet clinical annotations.

Joint hypermobilityRenal insufficiencyProteinuriaStrabismusOptic atrophyHypotoniaChoreoathetosisProfound intellectual disabilityAbnormal retinal pigmentationAbnormal retinal vascular morphologyGlomerulopathyWide mouthNarrow faceMandibular prognathiaMacrotiaVisual impairmentSpasticitySpastic diplegiaHyperreflexiaSandal gapShort statureAplasia/Hypoplasia of the cerebellumMalar prominenceHypoplasia of the zygomatic boneMask-like faciesCataractHypopigmented skin patchesScoliosisLarge earlobe

Classification & Codes

MeSH Code

C537739

Orphanet Code

ORPHA:2715
oculorenocerebellar syndrome
MeSHC537739
OrphanetORPHA:2715
Treatments0 drug(s)
Symptoms on record29 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO