oculoskeletodental syndrome

ORPHA: 557003

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with oculoskeletodental syndrome, sourced from HPO and Orphanet clinical annotations.

Short statureAbnormality of mucopolysaccharide metabolismNeurodevelopmental delayRetrognathiaEpicanthusConductive hearing impairmentSensorineural hearing impairmentWide nasal bridgeOligodontiaMicrodontiaMutismScoliosisDelayed skeletal maturationHypocalcemiaThoracic kyphosisHypoplasia of the capital femoral epiphysisHyperlordosisDepressed nasal bridgeEnamel hypoplasiaDysplastic corpus callosumFocal white matter lesionsShort 5th fingerThick nasal alaeAbnormal thalamus morphologyBroad columellaClinodactylyMetaphyseal dysplasiaNephrocalcinosisAbnormality of the dentitionCoarse facial featuresHearing impairmentGlaucomaDevelopmental cataractAbnormality of the frontal hairlineStrokeSpecific learning disabilityAbnormal facial shapeHypercalcemia

Classification & Codes

Orphanet Code

ORPHA:557003
oculoskeletodental syndrome
OrphanetORPHA:557003
Treatments0 drug(s)
Symptoms on record38 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO