Oliver–McFarlane syndrome

MeSH: C536554ORPHA: 3363

Overview

autosomal recessive disease characterized by trichomegaly, severe chorioretinal atrophy and multiple pituitary hormone deficiencies that has material basis in homozygous or compound heterozygous mutation in PNPLA6 on 19p13.2

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Oliver–McFarlane syndrome, sourced from HPO and Orphanet clinical annotations.

Retinal degenerationHypogonadismLong eyelashesPigmentary retinopathyHypothyroidismDecreased response to growth hormone stimulation testIntellectual disabilityAtaxiaGrowth delaySmall for gestational ageAlopeciaDelayed skeletal maturationNeonatal hyperbilirubinemiaSparse hairPeripheral neuropathyCryptorchidismMicropenisAbnormality of the dentitionMyopiaFrontal bossingMicrocephalySeizure

Classification & Codes

MeSH Code

C536554

Orphanet Code

ORPHA:3363
Oliver–McFarlane syndrome
MeSHC536554
OrphanetORPHA:3363
Treatments0 drug(s)
Symptoms on record22 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Oliver–McFarlane syndrome | OrphanDrug