olivopontocerebellar atrophy-deafness syndrome

ORPHA: 2732

Overview

medical condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with olivopontocerebellar atrophy-deafness syndrome, sourced from HPO and Orphanet clinical annotations.

Hearing impairmentStrabismusChorioretinal colobomaNystagmusOptic atrophySeizureAtaxiaHypertoniaHyperreflexiaVentriculomegalyCerebral cortical atrophyAbnormal speech patternEEG abnormalityOlivopontocerebellar atrophy

Classification & Codes

Orphanet Code

ORPHA:2732
olivopontocerebellar atrophy-deafness syndrome
OrphanetORPHA:2732
Treatments0 drug(s)
Symptoms on record14 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO