optic atrophy

MeSH: D009896ORPHA: 986731 Treatment Available

Overview

disorder characterized by loss of optic nerve fibers. It may be inherited or acquired. Acquired causes include ischemia, optic nerve neuropathy, glaucoma, trauma, radiation, brain tumors, and multiple sclerosis. It leads to vision disturbances

Available Treatments (1)

DrugFormStatusCountriesLead Time
idebenone
Orphan
oral tablet, 150 mgEMA Approved921d

Clinical Presentation

Signs and symptoms associated with optic atrophy, sourced from HPO and Orphanet clinical annotations.

Visual impairmentOptic atrophySensorineural hearing impairmentColor vision defectOphthalmoplegiaSensorimotor neuropathyTemporal optic disc pallorMorning glory anomalyModerately reduced visual acuityPtosisCentral scotomaAtaxiaGait disturbanceMyopathyHypogonadismCataractNystagmusDementiaHallucinationsDiabetes mellitusHypothyroidismSeizureSpasticitySpastic paraplegiaGlobal developmental delayHemiparesisCerebellar atrophyAreflexiaPes cavusMacrocytic anemiaDysphagiaMigraineBasal ganglia calcificationAbnormal periventricular white matter morphologySkeletal muscle atrophyMyalgiaScapular wingingAtrophy/Degeneration affecting the brainstemCorpus callosum atrophyDuane anomalyFeeding difficultiesFatigueWeakness of facial musculatureCognitive impairment

Classification & Codes

MeSH Code

D009896

Orphanet Code

ORPHA:98673
optic atrophy
MeSHD009896
OrphanetORPHA:98673
Treatments1 drug(s)
Symptoms on record44 signs
Statuspublished

Treatment Summary

Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO