organic acidemia

ICD-10: E70ORPHA: 68367

Overview

amino acid metabolic disorder that disrupts normal amino acid metabolism causing a building up of branched-chain amino acids

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

E70

Orphanet Code

ORPHA:68367
organic acidemia
ICD-10E70
OrphanetORPHA:68367
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO