osteoporosis-oculocutaneous hypopigmentation syndrome

MeSH: C536062ORPHA: 2786

Overview

Osteoporosis-oculocutaneous hypopigmentation syndrome is characterised by osteoporosis and congenital oculocutaneous hypopigmentation. Three cases have been described in the literature. The mode of inheritance appears to be autosomal recessive.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with osteoporosis-oculocutaneous hypopigmentation syndrome, sourced from HPO and Orphanet clinical annotations.

Abnormal retinal morphologyVisual impairmentMyopiaNystagmusPlatyspondylyOsteoporosisPallorHypopigmentation of the skinAlbinismKyphosisShort statureHypopigmentation of hair

Classification & Codes

MeSH Code

C536062

Orphanet Code

ORPHA:2786
osteoporosis-oculocutaneous hypopigmentation syndrome
MeSHC536062
OrphanetORPHA:2786
Treatments0 drug(s)
Symptoms on record12 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO