otofaciocervical syndrome 1

ORPHA: 2792

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with otofaciocervical syndrome 1, sourced from HPO and Orphanet clinical annotations.

High palateFull cheeksFacial asymmetryMacrotiaConductive hearing impairmentProtruding earAtresia of the external auditory canalAnteverted naresAbnormal clavicle morphologyIntellectual disabilityGlobal developmental delayHypertoniaHyperreflexiaAbnormal speech patternDelayed skeletal maturationScapular wingingShort staturePreauricular pitDepressed nasal bridgeAbnormal dermatoglyphicsRenal hypoplasia/aplasiaAbnormal antihelix morphologyDown-sloping shoulders

Classification & Codes

Orphanet Code

ORPHA:2792
otofaciocervical syndrome 1
OrphanetORPHA:2792
Treatments0 drug(s)
Symptoms on record23 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO