ovotesticular disorder of sex development

MeSH: D050090ORPHA: 2138

Overview

sexual ambiguity in which the individual possesses tissues from the ovary and the testis

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with ovotesticular disorder of sex development, sourced from HPO and Orphanet clinical annotations.

Abnormal morphology of female internal genitaliaAbnormal male internal genitalia morphologyCryptorchidismSmall scrotumHypospadiasBifid scrotumAmbiguous genitaliaAbnormality of the uterusDecreased fertilityPolycystic ovariesHypoplasia of penisTrue hermaphroditismAbnormal scrotal rugationUrogenital sinus anomaly

Classification & Codes

MeSH Code

D050090

Orphanet Code

ORPHA:2138
ovotesticular disorder of sex development
MeSHD050090
OrphanetORPHA:2138
Treatments0 drug(s)
Symptoms on record14 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
ovotesticular disorder of sex development | OrphanDrug