Pallister-Hall syndrome

ICD-10: D33.0MeSH: D054975ORPHA: 672

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Pallister-Hall syndrome, sourced from HPO and Orphanet clinical annotations.

Posteriorly rotated earsDownslanted palpebral fissuresPtosisMicrophthalmiaNatal toothRib fusionBrachydactylyPostaxial hand polydactylyIntrauterine growth retardationToe syndactylyAnal atresiaNail dysplasiaSkeletal dysplasiaHip dislocationHemivertebraeRadial bowingRadial head subluxationShort noseShort statureSupernumerary metacarpal bonesBilateral postaxial polydactylyGonadotropin deficiencySecondary growth hormone deficiencyPituitary hypothyroidismMicrotiaLaryngeal cleftPolydactyly affecting the 3rd fingerPolydactyly affecting the 4th fingerShort 4th metacarpalBroad thumbCentral adrenal insufficiencyAdrenocorticotropic hormone deficiency3-4 finger cutaneous syndactylyAbnormal basal ganglia MRI signal intensityHypopituitarismAbnormal prolactin levelMesoaxial polydactylyRecurrent upper and lower respiratory tract infectionsInguinal herniaCryptorchidismHypospadiasMicropenisEctopic kidneyUnilateral renal agenesisMicroglossiaCleft palateFacial grimacingMicroretrognathiaChoanal atresiaParoxysmal bursts of laughterPrecocious pubertyAdrenal hypoplasiaPanhypopituitarismGlobal developmental delayAbnormal corpus callosum morphologyCerebellar hypoplasiaHoloprosencephalyLarge for gestational ageUmbilical herniaVentricular septal defectAtrial septal defectPatent ductus arteriosusCoarctation of aortaBroad toeOverlapping toeAbnormal lung lobationThyroid hypoplasiaAtrioventricular canal defectMidline facial capillary hemangiomaPrimary adrenal insufficiencyDecreased testicular sizeBifid epiglottisFocal emotional seizure with laughingOligodactylyAuricular tagCleft lipSmall scrotumAmbiguous genitaliaTrigonocephalyIntellectual disabilityOligohydramniosTalipesRespiratory insufficiencyArrhinencephalyDistal arthrogryposisAplasia/hypoplasia of the uterusBilateral renal agenesisAplasia/Hypoplasia of the vaginaHydrometrocolposOsteochondromaScaphocephalyHypothalamic hamartomaRenal dysplasiaAccessory oral frenulumBifid uvulaMacrocephalyHypertelorismAtresia of the external auditory canalDepressed nasal ridgeAnteverted nares

Classification & Codes

ICD-10 Code

D33.0

MeSH Code

D054975

Orphanet Code

ORPHA:672
Pallister-Hall syndrome
ICD-10D33.0
MeSHD054975
OrphanetORPHA:672
Treatments0 drug(s)
Symptoms on record100 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO